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KMID : 1035620150030010086
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Allergy Asthma & Respiratory Disease
2015 Volume.3 No. 1 p.86 ~ p.89
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Pulmonary alveolar proteinosis in a 15-year-old girl
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경예찬:Kyung Ye-Chan
김지현:Kim Ji-Hyun/김홍관:Kim Hong-Kwan/한정호:Han Joung-Ho/안강모:Ahn Kang-Mo
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Abstract
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Pulmonary alveolar proteinosis (PAP) is a diffuse lung disease characterized by the accumulation of lipoproteins derived from surfactants in the distal air space. The lack of granulocyte macrophage colony-stimulating factor is believed to contribute to macrophage dysfunction and the impaired processing of surfactants. Because the prevalence of PAP in the general population is less than 1 in 200,000, and the typical age at presentation is 35 to 50 years, PAP is a very rare disease in children. To the best of our knowledge, there has been no Korean report on PAP in children. We describe here a patient who was diagnosed with PAP at the aged 15 years.
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KEYWORD
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Pulmonary alveolar proteinosis, Child
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